Abstract Rosai dorfman destombes disease (RDD) is a rare histiocytic disease primarily affecting the lymph nodes and soft tissues, predominantly observed in the younger male population of African descent. The exact etiology of the disease remains unknown, but it is believed to involve genetic mutations and reactive inflammatory reactions. We report the case of a 5-year-old male patient who is medically fit except for complaints of recurrent tonsillitis, ear pain, and hearing loss. The lab investigation was significant for tachycardia and elevated sodium (Na) levels. Computerized tomography and magnetic resonance imaging scans were done on the patient. Craniectomy was undertaken, and the lesion was surgically excised. The final diagnosis was made after fine-needle aspiration, which confirmed the diagnosis of (RDD). This case highlights the importance of always considering the occurrence of more than one pathology at once. Surgical excision remains the fundamental treatment, but steroids, radiotherapy, and chemotherapy are also available options.
AlDughaither et al. (Fri,) studied this question.
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