Fontan patients experience progressive kidney dysfunction and glomerular injury despite eGFR<sub>cr</sub> levels, due to decreased intrarenal compliance and reduced muscle mass.
Standard eGFRcr may underestimate kidney dysfunction in Fontan patients, who exhibit unique intrarenal hemodynamics including decreased compliance and continuous venous flow.
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FARD involves a progressive decline in kidney function and glomerular injury. eGFRcr masks kidney dysfunction in Fontan patients due to reduced muscle mass. Fontan intrarenal hemodynamics demonstrate decreased venous and arterial compliance. Moreover, continuous intrarenal venous flow persists in Fontan patients.
Hassel et al. (Tue,) reported a other. Fontan patients experience progressive kidney dysfunction and glomerular injury despite eGFR<sub>cr</sub> levels, due to decreased intrarenal compliance and reduced muscle mass.