INTRODUCTION: The incidence of multiple primary malignancies has increased owing to advances in cancer screening and treatment. However, cases involving five distinct primary cancers remain extremely rare. Intraductal papillary mucinous neoplasms (IPMNs) are known to be associated with extrapancreatic malignancies. We report a very uncommon case of quintuple primary cancers, including noninvasive intraductal papillary mucinous carcinoma (IPMC), and discuss its clinical implications.
Mori et al. (Thu,) studied this question.