This case shows the rarity of Malignant Proliferating Trichilemmal Tumor (MPTT) as well as its aggressive behavior as an adnexal tumor with metastatic potential, requiring early diagnosis and excision. MPTT may occur in younger patients and at atypical sites; malignant transformation should be suspected in long-standing trichilemmal lesions. This case underscores the need for more extensive studies on MPTT to better understand its epidemiology, associated systemic conditions, diagnostic evaluation, and therapeutic strategies. Early recognition and treatment are essential to prevent recurrence and metastasis.
Shrestha et al. (Wed,) studied this question.