INTRODUCTION: Biliary mucinous cystic neoplasm (MCN) is a cystic tumor characterized by ovarian-like stroma and is recognized as a neoplasm with the potential for invasive carcinoma. While MCNs predominantly occur in the pancreas, primary occurrence in the extrahepatic bile duct is exceedingly rare. Most reported cases are diagnosed postoperatively due to the lack of specific clinical symptoms, the difficulty in preoperative differentiation from other cystic diseases, such as intraductal papillary neoplasm of the bile duct, and the strict requirement of pathological evaluation for definitive diagnosis. Here, we report a case of primary extrahepatic biliary MCN that was strongly suspected preoperatively using multimodal imaging and treated with robotic surgery.
Shimogata et al. (Thu,) studied this question.