Why the study?
Current PAH risk stratification models are mainly derived from idiopathic PAH cohorts and are not automatically applicable to PAH associated with congenital heart disease, particularly Eisenmenger syndrome.
Population
Adult patients with PAH-CHD, mainly those with Eisenmenger syndrome
Design
Scientific statement
Authors
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Supports tailored prognostication in PAH-CHD; extends generic PAH models with CHD-specific factors.
This scientific statement proposes a tailored, comprehensive risk stratification model for patients with PAH-CHD, particularly Eisenmenger syndrome, addressing the limitations of applying idiopathic PAH models to this population.
D’Alto et al. (2026) studied this question.
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