Carcinoma of the Bartholin gland is a rare malignant tumor of the female genital tract, subcategorized within primary carcinomas of the vulva. The histopathological variant adenoid cystic carcinoma is extremely rare. There is no specific, consensus treatment for this pathology, but the gold standard is surgical removal. We present the case of a 30-year-old female patient with a history of Barrett's esophagus, who underwent specific treatment and presented with a lesion in the right vulvar region that had been causing moderate pain and localized itching for several months. She underwent surgery: right hemivulvectomy plus inguinal lymphadenectomy with a histopathological result of adenoid cystic carcinoma of the Bartholin's gland. Adenoid cystic carcinoma of the Bartholin's gland is a rare pathology with low incidence and unknown etiology. Diagnosis requires a combination of clinical, imaging, and histopathological aspects, and its treatment is currently controversial and nonspecific.
Bombon et al. (2026) studied this question.