Pulmonary underdevelopment is a rare congenital malformation typically identified in the pediatric population, incorporating a spectrum of pulmonary developmental disorders, including agenesis, aplasia, and hypoplasia of the lung.For diagnostic purposes chest x-rays are used as initial modality while, Contrast-Enhanced Computed Tomography and Computed Tomography angiogram are for confirming the diagnosis and specifying the anomaly extent. Right-sided anomaly is rare, often associated with VACTERL anomalies. We observed five cases of pulmonary underdevelopment, with four patients demonstrating right-sided involvement. A series of five pediatric patients underwent Contrast-Enhanced Computed Tomography (CECT) for evaluation of various forms of congenital pulmonary underdevelopment. Two patients, aged 12, and 21 months, had right-sided Type I (pulmonary agenesis). Type II (aplasia) was observed in 1.5 and 21-month-old child, while Type III (hypoplasia) was identified in a nine-month-old with right-sided involvement. Notably, the youngest of these exhibited features of VACTERL association, including a horseshoe kidney and kyphoscoliotic deformity. Encountering rare presentations of already uncommon disorders highlights the essential role of diagnostic modalities in today’s rapidly evolving medical practice.
Hameed et al. (Mon,) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: