Coordinated perioperative management of a child with Down syndrome and dual pacemakers enabled successful diaphragm pacer implantation and improved respiratory function without complications.
Multidisciplinary collaboration and coordinated pacemaker reprogramming are essential for safe perioperative management when implanting a diaphragm pacer in a patient with an existing abdominal cardiac pacemaker.
Down syndrome is associated with multisystem comorbidities complicating perioperative care, including cervical spine instability, airway abnormalities, and cardiac conduction defects. We report the case of a child with Down syndrome, high cervical myelopathy, progressing quadriplegia, and an abdominal cardiac pacemaker undergoing laparoscopic diaphragm pacer implantation. Management required advanced airway planning and coordinated pacemaker reprogramming to prevent device interference and arrhythmia. Continuous electrophysiologic monitoring was maintained throughout the procedure. The patient tolerated implantation without complication and achieved improved respiratory function with decreased ventilatory dependence. This case emphasizes the importance of multidisciplinary collaboration when multiple pacing systems coexist.
Johnson et al. (2026) studied this question. Coordinated perioperative management of a child with Down syndrome and dual pacemakers enabled successful diaphragm pacer implantation and improved respiratory function without complications.
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