Superior mesentery artery aneurysm with thrombosis and proximal stenosis in a case with Ehlers–Danlos syndrome

Introduction: Visceral arterial aneurysms are very rare in the pediatric patient population and might be associated with connective tissue disorders. Case Report: In this report, we present a 14-year-old male case with a superior mesenteric artery aneurysm with Ehlers–Danlos syndrome detected with computed tomography (CT) angiography. The patient had a history of scoliosis surgery associated with Ehlers–Danlos syndrome. A superior mesenteric artery aneurysm was detected along with a distal partial thrombosis and proximal stenosis. The patient was deceased 24 hours after admission to emergency room (ER) due to a generalized intestinal infarct. Conclusion: Visceral arterial aneurysms are very rare and associated complications might be fatal in the child population. Computed tomography (CT) angiography imaging provides a fast and accurate diagnosis and can delineate additional prognostic findings.