A Complex Case of Berry Syndrome following Transcatheter Pulmonary Valve Injury

Berry syndrome is a rare and complex congenital cardiac disease consisting of a constellation of anomalies including aortopulmonary window, anomalous origin of the right pulmonary artery from the ascending aorta, and interrupted aortic arch. Surgical treatment is typically performed in the first week or two after birth in patients with low-risk factors. Bilateral pulmonary artery banding as a stage to complete repair has been offered to neonates with prohibitive early surgical risks. We present a patient with Berry syndrome who underwent initial palliation with bilateral pulmonary artery banding followed by percutaneous transcatheter ductal stent insertion which led into pulmonary valve injury and severe pulmonary insufficiency needing urgent complete surgical repair.