Kaposiform haemangioendothelioma causing complete jejunal obstruction in a neonate: an unexpected intraoperative finding

Kaposiform haemangioendothelioma (KHE) is a rare vascular neoplasm that is seen most commonly on the extremities, head and neck or trunk. We present a case of a newborn baby boy who went to theatre for proximal bowel obstruction on day one of life. A large vascular malformation was encountered and the patient received a gastrostomy and a jejunostomy to keep the patient safe while allowing further investigations. Following a multi-disciplinary-team approach, the mass was resected and the histology confirmed KHE causing complete obstruction of the gastrointestinal tract. We summarise the key factors in clinical diagnosis, workup and recent treatment options for patients with this condition.