Treatment of systemic sclerosis-associated pulmonary hypertension with and without interstitial lung disease and its impact on survival: a large cohort study of the German network for systemic sclerosis

Puntos clave

• To investigate the effects of pulmonary hypertension treatment on survival outcomes in systemic sclerosis patients with and without interstitial lung disease.
• Analyzed a large cohort of systemic sclerosis patients.
• Evaluated treatment strategies involving pulmonary hypertension combination therapy.
• Assessed the severity of interstitial lung disease in patients.
• Examined survival outcomes associated with different treatment approaches.
• Combination therapy for pulmonary hypertension is feasible for SSc patients.
• Treatment does not worsen survival in pulmonary hypertension patients with mild interstitial lung disease.
• Severity of interstitial lung disease influences treatment outcomes.

Resumen